ASS1 Polyclonal Antibody | G-AB-06266

ASS1 Polyclonal Antibody | G-AB-06266 | Gentaur Antibodies

Overview: ASS1 is a rate-limiting enzyme in the urea cycle. Citrullinemia type I is an autosomal recessive disorder that is caused by a deficiency of the urea cycle enzyme argininosuccinate synthetase (ASS1) . Deficiency of ASS1 shows various clinical manifestations encompassing severely affected patients with fatal neonatal hyperammonemia as well as asymptomatic individuals with only a biochemical phenotype.

Category Type: Polyclonal Antibody

Research Areas: Cancer, Metabolism, Signal Transduction

Synonyms: Argininosuccinate synthase 1, Argininosuccinate synthase, Argininosuccinate synthetase 1, ASS, Ass-1, ass1, ASSA, ASSY, Citrulline aspartate ligase, Citrulline--aspartate ligase, CTLN1

Reactivity: Human, Mouse, Rat

Host: Rabbit

Isotype: IgG

Gene ID:

Accession #: BC021676

Clonality: Polyclonal

Immunogen: Fusion protein of human ASS1

Clone #:

Conjugation: Unconjugated

Swissprot: P00966

Santa Cruz:

Calculated MW: 47 kDa

Observed MW: Refer to figures

Concentration: 0.4 mg/mL

Buffer: PBS with 0.05% NaN3 and 40% Glycerol, pH7.4

Purification method: Antigen affinity purification

Application: WB, ELISA

Dilution: WB 1:500-1:2000, ELISA 1:5000-1:10000

Storage: Store at -20°C. Avoid freeze / thaw cycles.

ASS1 Polyclonal Antibody DataSheet