PEX12 Polyclonal Antibody | G-AB-09297

PEX12 Polyclonal Antibody | G-AB-09297 | Gentaur Antibodies

Overview: This gene belongs to the peroxin-12 family. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS) .

Category Type: Polyclonal Antibody

Research Areas:

Synonyms: PEX12, PAF-3, PBD3A

Reactivity: Human

Host: Rabbit

Isotype: IgG

Gene ID: 5193

Accession #:

Clonality:

Immunogen: Recombinant fusion protein of human PEX12 (NP_000277.1) .

Clone #:

Conjugation: Unconjugated

Swissprot: O00623

Santa Cruz:

Calculated MW: 40 kDa

Observed MW: 41 kDa

Concentration: 1 mg/mL

Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3

Purification method: Affinity purification

Application: WB

Dilution: WB 1:500-1:2000

Storage: Store at -20°C. Avoid freeze / thaw cycles.

PEX12 Polyclonal Antibody DataSheet